Clinicaly is characterized by hypoplasia of enamel and dentine in teeth badly formed with size and form altera. Here are links to possibly useful sources of information about regional odontodysplasia. Regional odontodysplasia is a rare developmental anomaly involving dental tissues. A rare localised developmental defect of teeth, which is more common in females, affecting enamel, dentin and pulp of teethespecially permanent teethresulting in an increased risk of caries and periapical inflammation. Case report generalised versus regional odontodysplasia. A localized arrested tooth development which appears to involve most commonly the anterior teeth, usually on one side of the midline. The affected teeth are usually small with atypical morphology with yellow or brown discoloration. Histologically, almost all dental tissues are altered. This page is about the various possible words that rhymes or sounds like odontodysplasia. Regional odontodysplasia, or ghost teeth, is a dental abnormality derived from both epithelial and mesenchymal components of the tooth bud. An unusual case of regional odontodysplasia, international. This case presents several common clinical and radiological features related to the regional odontodysplasia.
How to cite this article scientific research publishing. Diagnosis, transitional management, and longterm followup a report of 2 cases mostafaibrahimmostafa, 1 nehadsamirtaha, 2 andmennatallahismailmehrez 1 department of orodental genetics, national research centre, tahrir street, dokki, cairo, egypt. Intraoral view of the right quadrant of the patient with regional odontodysplasia. Radiographic images of the involved teeth show a ghostlike appearance because enamel and dentin are hypoplastic and hypocalcified. Regional odontodysplasia bv thimma reddy 1, kk vinay reddy 2, b sunil 3, r pujita 3, k kiran 3, kr kranthi 4 1 professor and head, department of pedodontics and preventive dentistry, mamata dental college and hospital, giri prasad nagar, khammam, andhra pradesh, india 2 professor and head, department of oral medicine and radiology, mamata dental college and hospital, giri. Information and translations of odontodysplasia in the most comprehensive dictionary definitions resource on the web. Both parents reported no previous history of tooth or genetic anomalies on either side of the family. If you do not see its contents the file may be temporarily unavailable at the journal website or you do not have a pdf plugin installed and enabled in your browser. Caso 4 volpato l, botelho g, casela l, borges a, silva k. Regional odontodysplasia ro is a rare developmental anomaly involving both mesodermal and ectodermal dental components in a group of contiguous teeth 8. Regional odontodysplasia is a rare idiopathic condition involving adjacent teeth.
Dec 21, 2016 regional odontodysplasia rod is uncommon developmental anomaly, which tends to be localised and involves the ectodermal and mesodermal tooth components. The regional odontodysplasia, also referred as odontogenic dysplasia, is a rare condition which has been described as an alteration of the dental development affecting the mineralized structures of both the permanent and deciduous teeth, and it has been associated with retardation in the eruption of the affected teeth, gum edema, hydrocephalus and epidermal. Regional odontodysplasia ro is an unusual, nonhereditary anomaly of the dental hard tissues with characteristic clinical, radiographic and histological findings. Case report regional odontodysplasia with generalised enamel defect a. Genetic and rare diseases information center gard po box 8126, gaithersburg, md 208988126 tollfree. This work and the related pdf file are licensed under a creative commons attribution 4. This condition was probably first described by hitchin 12 1934. Regional odontodysplasia with generalised enamel defect. Use it for writing poetry, composing lyrics for your song or coming up with rap verses. Regional odontodysplasia is a rare developmental anomaly of dental hard tissues. Here we present a case of a 7yearold japanese girl with regional odontodysplasia af fecting tooth numbers 24, 25, 26, and 27.
Clinically, ro affects the primary and permanent dentition in the. The regional odontodysplasia is a relatively rare developmental anomaly 16. Regional odontodysplasia regional odontodysplasia ferguson, j. Regional odontodysplasia ro is a rare dental anomaly involving both dentitions, mostly teeth of one quadrant. The cause of the condition is unknown and this is therefore best regarded as idiopathic. Odontodysplasia definition of odontodysplasia by medical. Case report regional odontodysplasia with generalised enamel. Despite the dif ferences between regional odontodysplasia and singular odontodysplasia, the histologie similarities in these two cases support a common cause. It can be localised or generalised, isolated or part of a syndrome.
The regional odontodysplasia, also referred as odon togenic dysplasia, is a rare condition which has been described as an alteration of the dental development affecting the mineralized structures of both the per manent and deciduous teeth, and it has been associ ated with retardation in the eruption of the affected. Many authors however, credit to mccall and wald 14 1947 the first report of this condition, showing only radiographic features. The treatment of ro is controversial and varies according to the individual patient. Regional odontodysplasia rod is uncommon developmental anomaly, which tends to be localised and involves the ectodermal and mesodermal tooth components. If you have problems viewing pdf files, download the latest version of adobe reader. Learn more about odontodysplasia from related diseases, pathways, genes and ptms with the novus bioinformatics tool. We present a rare case of a developmental anomaly called regional odontodysplasia or ghost teeth in a 12yearold indian girl.
Pdf the purpose of this article is to report some unusual characteristics related to gender, location and manifestations of severe regional. Case report regional odontodysplasia with generalised. Regional odontodysplasia of the deciduous and permanent teeth. Regional odontodysplasia is a developmental abnormality of teeth, usually localized to a certain area and nonhereditary. Its prevalence is reported to be less than 1000 and only about 140 cases have been reported in the literature up to the time of this study 6. A gingival swelling is sometimes associated with the affected teeth. This layer, called the ectoderm, develops into the skin, hair, nails, teeth, and eyes. Since there is no consensus in the literature regarding the etiology of dentin dysplasia and considering that this is a rare defect of dentin development, case reports can be useful to help elucidating and understanding some aspects related to. Periapical radiograph of tooth 11 showing amorphous calcification in the coronal half of the pulp chamber.
Regional odontodysplasia is a rare dental anomaly affecting both primary and adult dentitions in the maxilla or mandible or both jaws, whilst involvement of the maxilla is more common 12. Toumba 2 oral health department, sultan qaboos university hospital, sultan qaboos university, muscat, oman paediatric dentistry, leeds dental institute, university of leeds, leeds, uk correspondence should be addressed to a. A fiveyearold female was referred to department of child dental health at the leeds dental institute regarding malformed primary teeth. Regional odontodysplasia ro is a rare tooth anomaly. The enamel, dentin, and pulp of teeth are affected, and on radiographs the teeth are described as ghost teeth references. Regional odontodysplasia ro is a rare developmental anomaly involving both mesodermal and ectodermal dental components in a group of contiguous teeth. This pattern of distribution does not appear to have been reported previously and the extent of involvement poses problems for the long. Jul 08, 2014 educational video made by unmc college of dentistry class of 2016 dental students. The characteristic findings are discolored soft teeth accompanied by gingivitis, swelling or abscess. Regional odontodysplasia is a rare localized developmental disorder of dental origin which affects the primary and permanent. Regional odontodysplasia, australian dental journal 10.
The enamel, dentin, dental pulp, degenerating enamel organ, and dental follicle are all affected. This case is unusual in that it involved the mandibular dentition. Regional odontodysplasia is an uncommon, nonhereditary developmental dental disorder of unknown etiology, which should be early detected. Panoramic radiograph showing a dysplastic maxillary central incisor and teeth with a ghostlike appearance in the mandibular right quadrant. The condition affects the dentin and enamel of a group of adjacent teeth. Regional odontodysplasia of the deciduous and permanent. Regional odontodysplasia thimma reddy b v, vinay reddy k k. The most common root malformations in humans arise from either developmental disorders of the root alone or disorders of radicular development as part of a general tooth dysplasia. Ideal sources for wikipedia s health content are defined in the guideline wikipedia. Case report shiuyin cho, bds, mds, fracds abstract regional odontodysplasia is an uncommon developmental anomaly affecting a localized area of the dentition. However, in this case the mandible was unilaterally involved. This paper compares a regional odontodysplasia case with. Regional odontodysplasia mehta d n, bailoor d, patel b j. Frontiers malformations of the tooth root in humans.
Scientific research publishing is an academic publisher with more than 200 open access journal in the areas of science, technology and medicine. Report of a case in the mandible crossing the midline. It affects the primary and permanent dentitions in the maxilla and mandible or both jaws. The cause of odontodysplasia will remain ques tionable until this organizer influence can be determined and research into tooth development has advanced enough to answer these questions. Regional odontodysplasia herald scholarly open access. An unusual feature, only twice previously described in the world literature of fifty. Radiographic images of the involved teeth show a ghostlike appearance. As suggested by its name, dermatoodontodysplasia is characterized by skin and dental problems. The regional odontodysplasia has been associated with retardation in the eruption of the affected teeth 2,19,28 and gum swelling 1,2,19,28,29, vascular nevus 3,30,31 and hydrocephfalus 32,33. The enamel, dentin, and pulp of teeth are affected, and on radiographs the teeth are described as ghost teeth. Enamel and dentin are hypomineralised and hypoplastic, so that the ghost teeth appear shadowy in radiographs with wide pulp chambers. Educational video made by unmc college of dentistry class of 2016 dental students.
On examination, the patient had a deficient maxilla on the right side leading to facial asymmetry. Regional odontodysplasia has been predominantly described in the maxilla and in women, however these three cases are in boys and two of them occured in the mandible. Regional odontodysplasia is a rare developmental dental anomaly and the prevalence of this condition is still not definitely clear since the studies have mainly been based on the case reports 15. The affected teeth are often grossly malformed and develop abscess soon after eruption. There is no predilection for race, but females are more likely to get regional odontodysplasia. One hundred and seventy six cases of regional odontodysplasia have been published todate. General information also called ghost teeth it is an unusual development anomaly in which ectodermal and mesodermal tooth component are affected it is a localised arrest in tooth development in this condition all the elements of tooth are hypocalcified and hypoplastic. The presence of an abscess in relation to the lower right first permanent molar, in the absence of deep. This paper reports a case of ro affecting the permanent. Conservative management of regional odontodysplasia. On examination 64, 74, and 72 had localised hypomineralized enamel defect. Ghost teeth, odontogenesis imperfecta, arrested tooth development etiology. Regional odontodysplasia ro is a rare condition characterized by distinctive clinical, radiographic and microscopic findings. Thimma reddy bv, vinay reddy kk, sunil b, pujita r, kiran k, kranthi kr.
The anamnesis showed good general health, no history of dental or facial trauma and no previous orthodontic treatment. For language access assistance, contact the ncats public information officer. Regional odontodysplasia is an uncommon developmental anomaly affecting a local ized area of the dentition. The regional odontodysplasia, also referred as odontogenic dysplasia, is a rare condition which has been described as an alteration of the dental development affecting the mineralized structures of both the permanent and deciduous teeth, and it has been associated with retardation in the eruption of the affected teeth, gum edema, hydrocephalus and epidermal nevus syndrome. Intraoral view of the patient with regional odontodysplasia. Rarely, the recognition of regional odontodysplasia, a rare. The affected teeth are often grossly malformed and develop. Clinical management of regional odontodysplasia openventio.
Regional odontodysplasia is a localized disorder of tissues of dental origin resulting in characteristically bizarre clinical and radiographic appearances. It is more frequent in women than in men, and the maxilla is affected twice as often as the mandible 2. Regional odontodysplasia is a rare and unique dental developmental anomaly that affects tooth morphogenesis. Large pulp chambers and root canals with thin enamel and dentin.
After their publication in 2004, other 6 cases were retrieved from a pubmed database search until the present moment. Findings of clinical and radiographic examinations were consistent with those of generalised odontodysplasia. It is presumed to be the result of a developmental disturbance that locally affects the odontogenic ectodermal and mesodermal tissues. Regional odontodysplasia is an uncommon developmental abnormality of teeth, usually localized to a certain area of the mouth.
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